Stargardt disease (STGD) is the most common childhood recessively inherited macular dystrophy. The condition has a genetic basis due to mutations in the ABCA4gene, and results from the accumulation of visual cycle kinetics-derived byproducts in the retinal pigmented epithelium (RPE) with secondary photoreceptor dysfunction.
In FFA. Choroidal silence or diffuse choroidal hypoflourescence is pathognomonic and in advanced stage there is macular atrophy that may have the (Bull\'s eye) appearance in color and or FFA. FAF revealed corresponding hypoautoflourescence due to RPE atrophy.